Table 5. [IV Ammonia Scavenger Therapy Protocol]. - GeneReviews®

Deficiency	Patient Weight	Components of Infusion Solution	Dosage Provided	Administration
CPS & OTC	0-20 kg	2.5 mL/kg	2.0 mL/kg	250 mg/kg	250 mg/kg	200 mg/kg	Loading ³ Maintenance ⁴
ASS1 & ASL	2.5 mL/kg	6.0 mL/kg	250 mg/kg	250 mg/kg	600 mg/kg
CPS & OTC	>20 kg	55 mL/m²	2.0 mL/kg	5.5 g/m²	5.5 g/m²	4000 mg/m²
ASS1 & ASL	55 mL/m²	6.0 mL/kg	5.5 g/m²	5.5 g/m²	12000 mg/m²

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Deficiency	Patient Weight	Components of Infusion Solution		Dosage Provided			Administration
Deficiency	Patient Weight	Sodium phenylacetate& sodium benzoate ^1, 2	Arginine HCl injection, 10% ²	Sodium phenyl-acetate	Sodium benzoate	Arginine HCl	Administration
CPS & OTC	0-20 kg	2.5 mL/kg	2.0 mL/kg	250 mg/kg	250 mg/kg	200 mg/kg	Loading ³ Maintenance ⁴
ASS1 & ASL	0-20 kg	2.5 mL/kg	6.0 mL/kg	250 mg/kg	250 mg/kg	600 mg/kg
CPS & OTC	>20 kg	55 mL/m²	2.0 mL/kg	5.5 g/m²	5.5 g/m²	4000 mg/m²
ASS1 & ASL	>20 kg	55 mL/m²	6.0 mL/kg	5.5 g/m²	5.5 g/m²	12000 mg/m²